Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome
نویسندگان
چکیده
A 7-year-old boy presented at our hospital with syncope. At birth, electrocardiography had shown a long QT interval with torsade de pointes (TdP). Congenital long QT syndrome (LQTS) had been diagnosed by genetic testing, and was successfully controlled with oral propranolol. At age 7, TdP had recurred with syncope. Electrocardiography revealed a prominent long QT interval with T-wave alternans. The propranolol dose was increased, but TdP remained uncontrolled. A cardioverter-defibrillator (ICD) was implanted epicardially, and TdP completely resolved with atrial pacing. We report this rare case of ICD implantation in a child with LQTS.
منابع مشابه
Management of patients with long QT syndrome
I have read with great interest the case report entitled “Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome” by Sugiyama et al. in the latest issue of the journal [1]. The authors well presented a case of long QT syndrome managed using implantation of an epicardial shock electrode and dose titration of beta-blocker therapy. However, some imp...
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